Lymphangioma cicnmscriptum is a rare disease and the lesions are indistinguishable, clinically and histologically, from lymphangiectasis.
The only difference is that lymphangiectasis is usually bilateral and develops in adult or later life, ie, secondary to irradiation, surgical intervention or some malignancies, but lymphangioma circumscriptum is congenital disease er develops soon after birth.
The general pathology textbooks contain very little information about this interesting condition.
A case of the lymphangioma circumscriptum of left thigh in a 17-year old woman was reported, which was characteristic of clinical manifestation of deep seated and grouped vesicles resembling frog spawn which were purplish in color and tense in consistence.
Findings of routine examination were within normal limit.
The histological appearance of the epidermis showed slight hyperkeratosis, and acanthosis, cystically dilated and lymph vessels lined by a single layer of endothelium in the uppermost portion of epidermis. These lymph vessels contain, in addition to lymph, also some erythrocyte.
Treatment consists of complete excision and split thickness skin graft.
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